EC PAEDIATRICS Case Report Primary Empty Sella Syndrome and Central Precocious Puberty in a Boy with Recurrent Headache. A Case Report

نویسنده

  • Simon Kayemba-Kay’s
چکیده

Central precocious puberty (CPP) is commoner in girls in comparison to boys. Its Causes are idiopathic in over 80% girls while being secondary to central nervous system pathologies in 80% boys. CPP in association with empty sella syndrome, a condition often linked with idiopathic intracranial hypertension, is rare. We report a case of a boy with CPP and recurrent headaches in whom empty sella was diagnosed. Management consisted of GnRH analog therapy. Follow-up (clinical, ophthalmologic, and repeat MRI) remained uneventful. ES as cause of CPP must be known and close surveillance considered as secondary complications may occur.

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تاریخ انتشار 2017